Research Output 1962 2020

2019

Scurvy: a rare case in an adult

Joshi, R., Gustas-French, C. N., Fanburg-Smith, J., Helm, K. & Flemming, D., Jun 1 2019, In : Skeletal Radiology. 48, 6, p. 977-984 8 p.

Research output: Contribution to journalArticle

Scurvy
Exanthema
Hemorrhage
Anti-Bacterial Agents
Cellulitis
1 Citation (Scopus)

Semaphorin4A causes loss of mature oligodendrocytes and demyelination in vivo

Chiou, B., Neely, E., Kallianpur, A. & Connor, J., Feb 8 2019, In : Journal of Neuroinflammation. 16, 1, 28.

Research output: Contribution to journalArticle

Open Access
Oligodendroglia
Demyelinating Diseases
Corpus Callosum
Myelin Sheath
Cerebrospinal Fluid

Sensory Eating Problems Scale (SEPS) for children: Psychometrics and associations with mealtime problems behaviors

Seiverling, L., Williams, K., Hendy, H. M., Adams, W., Yusupova, S. & Kaczor, A., Feb 1 2019, In : Appetite. 133, p. 223-230 8 p.

Research output: Contribution to journalArticle

Psychometrics
Meals
Eating
Food
Touch
Adult Respiratory Distress Syndrome
Pediatrics
Pneumonia
Viruses
Viral Pneumonia

Sphingolipid metabolism determines the therapeutic efficacy of nanoliposomal ceramide in acute myeloid leukemia

Barth, B. M., Wang, W., Toran, P. T., Fox, T. E., Annageldiyev, C., Ondrasik, R. M., Keasey, N. R., Brown, T. J., Devine, V. G., Sullivan, E. C., Cote, A. L., Papakotsi, V., Tan, S. F., Shanmugavelandy, S. S., Deering, T. G., Needle, D. B., Stern, S. T., Zhu, J., Liao, J., Viny, A. D. & 7 others, Feith, D. J., Levine, R. L., Wang, H. G., Loughran, T. P., Sharma, A., Kester, M. & Claxton, D. F., Sep 10 2019, In : Blood Advances. 3, 17, p. 2598-2603 6 p.

Research output: Contribution to journalArticle

Open Access
Sphingolipids
Ceramides
Acute Myeloid Leukemia
Therapeutics

Spinal cord lesions in a pediatric patient with chronic kidney disease and review of literature: Answers

Tiwana, H., Patel, H., Asghar, S., Kumar, A. & Freeman, M., Jun 1 2019, In : Pediatric Nephrology. 34, 6, p. 1035-1036 2 p.

Research output: Contribution to journalArticle

Chronic Renal Insufficiency
Spinal Cord
Pediatrics

Spinal cord lesions in a pediatric patient with chronic kidney disease and review of literature: Questions

Tiwana, H., Patel, H., Asghar, S., Kumar, A. & Freeman, M., Jun 1 2019, In : Pediatric Nephrology. 34, 6, 1 p.

Research output: Contribution to journalArticle

Chronic Renal Insufficiency
Spinal Cord
Pediatrics

Stroke among cancer patients

Zaorsky, N. G., Zhang, Y., Tchelebi, L. T., Mackley, H. B., Chinchilli, V. M. & Zacharia, B. E., Dec 1 2019, In : Nature communications. 10, 1, 5172.

Research output: Contribution to journalArticle

Open Access
strokes
cancer
Stroke
Neoplasms
Epidemiology

Structural and Functional Determinants of Rodent and Human Surfactant Protein A: A Synthesis of Binding and Computational Data

Nalian, A., Umstead, T. M., Yang, C. H., Silveyra, P., Thomas, N. J., Floros, J., McCormack, F. X. & Chroneos, Z. C., Nov 7 2019, In : Frontiers in immunology. 10, 2613.

Research output: Contribution to journalArticle

Open Access
Pulmonary Surfactant-Associated Protein A
Rodentia
Alveolar Macrophages
varespladib methyl
Surface-Active Agents

Structural Basis of Colchicine-Site targeting Acylhydrazones active against Multidrug-Resistant Acute Lymphoblastic Leukemia

Cury, N. M., Mühlethaler, T., Laranjeira, A. B. A., Canevarolo, R. R., Zenatti, P. P., Lucena-Agell, D., Barasoain, I., Song, C., Sun, D., Dovat, S., Yunes, R. A., Prota, A. E., Steinmetz, M. O., Díaz, J. F. & Yunes, J. A., Nov 22 2019, In : iScience. 21, p. 95-109 15 p.

Research output: Contribution to journalArticle

Open Access
Colchicine
Tubulin
Precursor Cell Lymphoblastic Leukemia-Lymphoma
Tubulin Modulators
ATP-Binding Cassette Transporters

Subcutaneous C1 inhibitor for prevention of attacks of hereditary angioedema: Additional outcomes and subgroup analysis of a placebo-controlled randomized study

Li, H. H., Zuraw, B., Longhurst, H. J., Cicardi, M., Bork, K., Baker, J., Lumry, W., Bernstein, J., Manning, M., Levy, D., Riedl, M. A., Feuersenger, H., Prusty, S., Pragst, I., Machnig, T. & Craig, T., Aug 28 2019, In : Allergy, Asthma and Clinical Immunology. 15, 1, 49.

Research output: Contribution to journalArticle

Open Access
Hereditary Angioedemas
Complement C1 Inhibitor Protein
Placebos
Therapeutics
Hereditary Angioedema Types I and II

Surfactant protein A and D personalized medicine: A healthy day at the SP-A

Floros, J. & D'Ovidio, F., Jun 2019, In : Journal of Thoracic and Cardiovascular Surgery. 157, 6, p. e425

Research output: Contribution to journalLetter

Open Access
Pulmonary Surfactant-Associated Protein D
Pulmonary Surfactant-Associated Protein A
Precision Medicine
2 Citations (Scopus)

Surfactant protein A and D polymorphisms and methylprednisolone pharmacogenetics in donor lungs

Aramini, B., Geraghty, P., Lederer, D. J., Costa, J., DiAngelo, S. L., Floros, J. & D'Ovidio, F., May 2019, In : Journal of Thoracic and Cardiovascular Surgery. 157, 5, p. 2109-2117 9 p.

Research output: Contribution to journalArticle

Pulmonary Surfactant-Associated Protein D
Pulmonary Surfactant-Associated Protein A
Pharmacogenetics
Methylprednisolone
varespladib methyl
1 Citation (Scopus)

Survey of peer review programs among pediatric radiologists: report from the SPR Quality and Safety Committee

Iyer, R. S., Swenson, D. W., Anand, N., Blumfield, E., Chandra, T., Chavhan, G. B., Goodman, T. R., Khan, N., Moore, M. M., Ngo, T. D., Sammet, C. L., Sze, R. W., Vera, C. D. & Stanescu, A. L., Apr 1 2019, In : Pediatric Radiology. 49, 4, p. 517-525 9 p.

Research output: Contribution to journalReview article

Peer Review
Radiology
Pediatrics
Safety
Learning
5 Citations (Scopus)

Survival and Functional Outcomes in Boys with Cerebral Adrenoleukodystrophy with and without Hematopoietic Stem Cell Transplantation

Raymond, G., Aubourg, P., Paker, A., Escolar, M., Fischer, A., Blanche, S., Baruchel, A., Dalle, J. H., Michel, G., Prasad, V., Miller, W., Paadre, S., Balser, J., Kurtzberg, J., Nascene, D. R., Orchard, P. J. & Lund, T., Mar 1 2019, In : Biology of Blood and Marrow Transplantation. 25, 3, p. 538-548 11 p.

Research output: Contribution to journalArticle

Adrenoleukodystrophy
Hematopoietic Stem Cell Transplantation
Survival
Graft vs Host Disease
Confidence Intervals
1 Citation (Scopus)

Survival outcomes of allogeneic hematopoietic cell transplants with EBV-positive or EBV-negative post-transplant lymphoproliferative disorder, A CIBMTR study

Naik, S., Riches, M., Hari, P., Kim, S., Chen, M., Bachier, C., Shaughnessy, P., Hill, J., Ljungman, P., Battiwalla, M., Chhabra, S., Daly, A., Storek, J., Ustun, C., Diaz, M. A., Cerny, J., Beitinjaneh, A., Yared, J., Brown, V., Page, K. & 13 others, Dahi, P. B., Ganguly, S., Seo, S., Chao, N., Freytes, C. O., Saad, A., Savani, B. N., Woo Ahn, K., Boeckh, M., Heslop, H. E., Lazarus, H. M., Auletta, J. J. & Kamble, R. T., Oct 1 2019, In : Transplant Infectious Disease. 21, 5, e13145.

Research output: Contribution to journalArticle

Lymphoproliferative Disorders
Human Herpesvirus 4
Bone Marrow
Transplants
Survival

Susceptibility-weighted imaging of retinal hemorrhages in abusive head trauma

Thamburaj, K., Soni, A., Frasier, L., Tun, K. N., Weber, S. R. & Dias, M., Feb 7 2019, In : Pediatric Radiology. 49, 2, p. 210-216 7 p.

Research output: Contribution to journalArticle

Retinal Hemorrhage
Craniocerebral Trauma
Ophthalmoscopy
Intracranial Hemorrhages
Brain

Systemic timolol exposure following topical application to infantile hemangiomas

Pediatric Trials Network Steering Committee (See Acknowledgments for a listing of committee members.), Jan 1 2019, (Accepted/In press) In : Journal of the American Academy of Dermatology.

Research output: Contribution to journalArticle

Targeting IL-13Ra2 for effective treatment of malignant peripheral nerve sheath tumors in mouse models

Mrowczynski, O. D., Payne, R. A., Bourcier, A. J., Mau, C. Y., Slagle-Webb, B., Shenoy, G., Madhankumar, A. B., Abramson, S. B., Wolfe, D., Harbaugh, K. S., Rizk, E. B. & Connor, J. R., Jan 1 2019, In : Journal of neurosurgery. 131, 5, p. 1369-1379 11 p.

Research output: Contribution to journalArticle

Interleukin-13 Receptors
Neurilemmoma
Interleukin-13
Therapeutics
Survival

Teaching NeuroImages: A rare case of Jacobsen syndrome with global diffuse hypomyelination of brain

Patel, H., Kumar, A., Raymond, G. & Mainali, G., Apr 2 2019, In : Neurology. 92, 14, p. E1665-E1666

Research output: Contribution to journalComment/debate

Open Access
Jacobsen Distal 11q Deletion Syndrome
Teaching
Brain

Term Neonate Presenting with the Combined Occurrence of Mucolipidosis Type II and Leigh Syndrome

Speer, R. R., Ezeanya, U. C., Beaudoin, S., Glass, K. & Oji-Mmuo, C., Oct 2019, In : Journal of Pediatric Genetics.

Research output: Contribution to journalArticle

Leigh Disease
Mucolipidoses
Newborn Infant
Chromosomes, Human, Pair 12
Mitochondria
1 Citation (Scopus)

The association of early post-resuscitation hypotension with discharge survival following targeted temperature management for pediatric in-hospital cardiac arrest

for the Therapeutic Hypothermia after Pediatric Cardiac Arrest (THAPCA) Trial Investigators, Aug 2019, In : Resuscitation. 141, p. 24-34 11 p.

Research output: Contribution to journalArticle

Extracorporeal Membrane Oxygenation
Pediatric Hospitals
Heart Arrest
Resuscitation
Hypotension
1 Citation (Scopus)
Sickle Cell Anemia
Pulmonary Hypertension
Obstructive Sleep Apnea
Hypoxia
Sickle Hemoglobin

The author replies

Zaenglein, A., Jan 10 2019, In : New England Journal of Medicine. 380, 2, p. 199-200 2 p.

Research output: Contribution to journalLetter

The authors reply

Imber, D. A., Thomas, N. J. & Yehya, N., Jul 1 2019, In : Pediatric Critical Care Medicine. 20, 7, p. 693-694 2 p.

Research output: Contribution to journalLetter

The Combined Effects of Immediate and Delayed Positive Reinforcement to Increase Consumption of Solid Food: A Brief Report

Williams, K., Adams, W. & Creek, L., Nov 17 2019, In : Developmental Neurorehabilitation. 22, 8, p. 576-580 5 p.

Research output: Contribution to journalArticle

Food
Cues
Gastrostomy
Bites and Stings
Intellectual Disability
4 Citations (Scopus)

The effect of substantiated and unsubstantiated investigations of child maltreatment and subsequent adolescent health

Kugler, K. C., Guastaferro, K., Shenk, C. E., Beal, S. J., Zadzora, K. M. & Noll, J. G., Jan 1 2019, In : Child Abuse and Neglect. 87, p. 112-119 8 p.

Research output: Contribution to journalArticle

Child Abuse
Propensity Score
Risk-Taking
HIV
Depression
Autologous Blood Transfusions
Oxidative Stress
Leukocytes
Lung
Blood Transfusion
medical student
teacher
Teaching
narrative
student

The glucose control resistance scale

Nikita, M. E., Hendy, H. M., Williams, K. E. & Mueller, P. L., Jun 2019, In : JCRPE Journal of Clinical Research in Pediatric Endocrinology. 11, 2, p. 118-124 7 p.

Research output: Contribution to journalArticle

Open Access
Family Conflict
Glucose
Body Image
Hemoglobins
Parents

The Healthy Champions program in Pennsylvania schools: Assessment, awareness, and improvement of school wellness

Francis, E., Hogentogler, R., Hoke, A., Buckley, J., Hwang, G., Lehman, E. & Kraschnewski, J. L., Dec 2019, In : Preventive Medicine Reports. 16, 101018.

Research output: Contribution to journalArticle

Open Access
Pediatric Obesity
Health Promotion

The Human Transient Receptor Potential Melastatin 2 Ion Channel Modulates ROS Through Nrf2

Bao, L., Festa, F., Freet, C. S., Lee, J. P., Hirschler-Laszkiewicz, I. M., Chen, S. J., Keefer, K. A., Wang, H. G., Patterson, A. D., Cheung, J. Y. & Miller, B. A., Dec 1 2019, In : Scientific reports. 9, 1, 14132.

Research output: Contribution to journalArticle

Open Access
Transient Receptor Potential Channels
Ion Channels
Cell Survival
NADP
NAD

Themes Depicted in Running-Related Films: An Opportunity for Co-Viewing and Active Mediation

Nelson, A., Patterson, K., Groff, A., King, T. S., Brady, J. & Olympia, R. P., Jun 1 2019, In : Clinical Pediatrics. 58, 7, p. 778-788 11 p.

Research output: Contribution to journalArticle

Running
Sports
Confidence Intervals
Adolescent Development
Child Development
Neonatal Abstinence Syndrome
Newborn Infant
Cohort Studies
Outpatients
Retrospective Studies
2 Citations (Scopus)

The Post-GWAS Era: How to Validate the Contribution of Gene Variants in Lupus

Fike, A. J., Elcheva, I. & Rahman, Z., Jan 1 2019, In : Current rheumatology reports. 21, 1, 3.

Research output: Contribution to journalReview article

Genome-Wide Association Study
Systemic Lupus Erythematosus
Genes
Computational Biology
Autoimmune Diseases

The role of microRNAs in chronic pseudomonas lung infection in Cystic fibrosis

Fesen, K., Silveyra, P., Fuentes, N., Nicoleau, M., Rivera, L., Kitch, D., Graff, G. & Siddaiah, R., May 1 2019, In : Respiratory Medicine. 151, p. 133-138 6 p.

Research output: Contribution to journalArticle

Pseudomonas Infections
MicroRNAs
Cystic Fibrosis
Lung
Pseudomonas aeruginosa

These Things Happen

Soni, A., Nov 12 2019, In : JAMA - Journal of the American Medical Association. 322, 18, p. 1767-1768 2 p.

Research output: Contribution to journalComment/debate

Open Access

The Transcriptional Signature of a Runner's High

Hicks, S. D., Jacob, P., Perez, O., Baffuto, M., Gagnon, Z. & Middleton, F. A., May 1 2019, In : Medicine and science in sports and exercise. 51, 5, p. 970-978 9 p.

Research output: Contribution to journalArticle

Endocannabinoids
MicroRNAs
Endorphins
Nerve Growth Factors
RNA

The World Database for Pediatric and Congenital Heart Surgery “A Call to Service for North American Congenital Heart Surgery Programs”

St. Louis, J. D., Timkovich, N., Lenderman, S., Jonas, R. A., Guleserian, K. J., Tchervenkov, C. I., Jacobs, J. P., Austin, E. H., Plunkett, M. D., Myers, J. L., Hraska, V., Sinha, P., O'Brien, J. E., Jacobs, M. L. & Kirklin, J. K., Jun 1 2019, In : Seminars in thoracic and cardiovascular surgery. 31, 2, p. 230-233 4 p.

Research output: Contribution to journalArticle

Congenital Heart Defects
Thoracic Surgery
Databases
Pediatrics
Therapeutics

Time-resolved FRET and NMR analyses reveal selective binding of peptides containing the LC3-interacting region to ATG8 family proteins

Atkinson, J. M., Ye, Y., Gebru, M. T., Liu, Q., Zhou, S., Young, M. M., Takahashi, Y., Lin, Q., Tian, F. & Wang, H. G., Jan 1 2019, In : Journal of Biological Chemistry. 294, 38, p. 14033-14042 10 p.

Research output: Contribution to journalArticle

Open Access
Autophagy
Nuclear magnetic resonance
Peptides
Proteins
GABA Receptors
1 Citation (Scopus)

TOM40 Targets Atg2 to Mitochondria-Associated ER Membranes for Phagophore Expansion

Tang, Z., Takahashi, Y., He, H., Hattori, T., Chen, C., Liang, X., Chen, H., Young, M. M. & Wang, H. G., Aug 13 2019, In : Cell Reports. 28, 7, p. 1744-1757.e5

Research output: Contribution to journalArticle

Open Access
Mitochondria
Membranes
Fluxes
Mitochondrial Proteins
Autophagy

Tools and methods for measuring implicit consumer cognition

Pogacar, R., Carpenter, T. P., Shenk, C. E. & Kouril, M., Apr 15 2019, Handbook of Research Methods in Consumer Psychology. Taylor and Francis Inc., p. 160-181 22 p.

Research output: Chapter in Book/Report/Conference proceedingChapter

Cognition

Tracking resident pre-rounding electronic health record usage

Krawiec, C., Marker, C., Stetter, C., Kong, L. & Thomas, N. J., Apr 15 2019, In : International Journal of Health Care Quality Assurance. 32, 3, p. 611-620 10 p.

Research output: Contribution to journalArticle

Electronic Health Records
Mechanical Ventilators
Critical Care
Patient Acuity
Workflow

Training teachers to implement physical activity: Applying social cognitive theory

Hivner, E. A., Hoke, A. M., Francis, E. B., Lehman, E. B., Hwang, G. W. & Kraschnewski, J., Jun 1 2019, In : Health Education Journal. 78, 4, p. 464-475 12 p.

Research output: Contribution to journalArticle

Exercise
Self Efficacy
Social Theory
Focus Groups
Randomized Controlled Trials

Transferrin and H-ferritin involvement in brain iron acquisition during postnatal development: impact of sex and genotype

Chiou, B., Neely, E. B., Mcdevitt, D. S., Simpson, I. & Connor, J., Jan 1 2019, (Accepted/In press) In : Journal of neurochemistry.

Research output: Contribution to journalArticle

Apoferritins
Sexual Development
Transferrin
Brain
Iron

Trauma and Post Traumatic Growth in Young Survivors of a Terrorist Attack: An Experiential Account of Supportive Interventions in a Tertiary Care Hospital in Pakistan

Nadeem, T., Asad, N., Khan, M. M., Siddiqui, S., Mahr, F., Hamid, S. N. & Pirani, S., Jan 1 2019, (Accepted/In press) In : Child Care in Practice.

Research output: Contribution to journalArticle

Pakistan
Tertiary Healthcare
Tertiary Care Centers
Survivors
trauma
1 Citation (Scopus)
Open Access
Hereditary Angioedemas
1 Citation (Scopus)

Trends in hospitalizations related to anaphylaxis, angioedema, and urticaria in the United States

Shrestha, P., Dhital, R., Poudel, D., Donato, A., Karmacharya, P. & Craig, T., Apr 2019, In : Annals of Allergy, Asthma and Immunology. 122, 4, p. 401-406.e2

Research output: Contribution to journalArticle

Angioedema
Urticaria
Anaphylaxis
Hospitalization
Age Groups

Trpm2 enhances physiological bioenergetics and protects against pathological oxidative cardiac injury: Role of Pyk2 phosphorylation

Miller, B., Wang, J. F., Song, J., Zhang, X. Q., Hirschler-Laszkiewicz, I., Santhanam, S., Tomar, D., Rajan, S., Feldman, A. M., Madesh, M., Sheu, S. S. & Cheung, J. Y., Sep 1 2019, In : Journal of Cellular Physiology. 234, 9, p. 15048-15060 13 p.

Research output: Contribution to journalArticle

Focal Adhesion Kinase 2
Phosphorylation
Energy Metabolism
Muscle Cells
Wounds and Injuries
5 Citations (Scopus)

TRPM2 in Cancer

Miller, B., Jun 1 2019, In : Cell Calcium. 80, p. 8-17 10 p.

Research output: Contribution to journalReview article

Cell Survival
Neoplasms
Neuroblastoma
Autophagy
Breast Neoplasms