Anomalous origin of the right coronary artery from the pulmonary artery in a neonate with turner syndrome and aortic arch hypoplasia

Research output: Contribution to journalArticle

Abstract

Anomalous origin of the right coronary artery from the pulmonary artery, a rare congenital cardiac defect, is typically not diagnosed during infancy. On the other hand, Turner syndrome is usually diagnosed early, and it is classically associated with bicuspid aortic valve and aortic coarctation. Individuals with Turner syndrome are also at increased risk for coronary artery anomalies. We present a case of anomalous right coronary artery from the pulmonary artery in a week-old neonate who also had Turner syndrome, patent ductus arteriosus, transverse aortic arch hypoplasia, and impaired ventricular function. Prostaglan-din therapy through the ductus increased the patient’s myocardial perfusion. Four months after corrective surgery, she was doing well. We discuss the reperfusion phenomenon in our patient’s case, as well as other considerations in this combination of congenital defects.

Original languageEnglish (US)
Pages (from-to)225-228
Number of pages4
JournalTexas Heart Institute Journal
Volume46
Issue number3
DOIs
StatePublished - Jun 2019

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Turner Syndrome
Thoracic Aorta
Pulmonary Artery
Coronary Vessels
Newborn Infant
Patent Ductus Arteriosus
Aortic Coarctation
Ventricular Function
Reperfusion
Perfusion
Therapeutics

All Science Journal Classification (ASJC) codes

  • Cardiology and Cardiovascular Medicine

Cite this

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title = "Anomalous origin of the right coronary artery from the pulmonary artery in a neonate with turner syndrome and aortic arch hypoplasia",
abstract = "Anomalous origin of the right coronary artery from the pulmonary artery, a rare congenital cardiac defect, is typically not diagnosed during infancy. On the other hand, Turner syndrome is usually diagnosed early, and it is classically associated with bicuspid aortic valve and aortic coarctation. Individuals with Turner syndrome are also at increased risk for coronary artery anomalies. We present a case of anomalous right coronary artery from the pulmonary artery in a week-old neonate who also had Turner syndrome, patent ductus arteriosus, transverse aortic arch hypoplasia, and impaired ventricular function. Prostaglan-din therapy through the ductus increased the patient’s myocardial perfusion. Four months after corrective surgery, she was doing well. We discuss the reperfusion phenomenon in our patient’s case, as well as other considerations in this combination of congenital defects.",
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