Arrhythmogenic Right Ventricular Dysplasia: Cardiomyopathy current opinions on diagnostic and therapeutic aspects

Franco Naccarella, Gerald Naccarelli, Rosella Fattori, Andrea Nava, Bortolo Martini, Domenico Corrado, Andrea Masotti, Mauro Gatti

Research output: Contribution to journalReview article

22 Citations (Scopus)

Abstract

Right Ventricular Dysplasia constitutes a genetic cardiomyopathy characterized by fibrous-adipose substitution of the right and rarely of the left ventricular myocardium. This disorder is associated with ventricular arrhythmias ranging from frequent ventricular ectopic beats, nonsustained and sustained ventricular tachycardia of left bundle branch morphology and sudden death. Therefore, the syndrome has been labelled Arrhythmogenic RVD Cardiomyopathy. Diagnostic criteria, preliminary genetic data, and clinical manifestations are summarized and critical addressed, using data from the literature and from our own experience. The most important aspects of the ECG in this syndrome are reviewed and stressed with particular attention to initial versus advanced clinical subsets. The typical anatomical abnormalities and biopsy or pathology material are presented.

Original languageEnglish (US)
Pages (from-to)8-16
Number of pages9
JournalCurrent Opinion in Cardiology
Volume16
Issue number1
DOIs
StatePublished - Jan 30 2001

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Arrhythmogenic Right Ventricular Dysplasia
Cardiomyopathies
Ventricular Premature Complexes
Ventricular Tachycardia
Sudden Death
Cardiac Arrhythmias
Myocardium
Electrocardiography
Pathology
Biopsy
Therapeutics

All Science Journal Classification (ASJC) codes

  • Cardiology and Cardiovascular Medicine

Cite this

Naccarella, Franco ; Naccarelli, Gerald ; Fattori, Rosella ; Nava, Andrea ; Martini, Bortolo ; Corrado, Domenico ; Masotti, Andrea ; Gatti, Mauro. / Arrhythmogenic Right Ventricular Dysplasia : Cardiomyopathy current opinions on diagnostic and therapeutic aspects. In: Current Opinion in Cardiology. 2001 ; Vol. 16, No. 1. pp. 8-16.
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Arrhythmogenic Right Ventricular Dysplasia : Cardiomyopathy current opinions on diagnostic and therapeutic aspects. / Naccarella, Franco; Naccarelli, Gerald; Fattori, Rosella; Nava, Andrea; Martini, Bortolo; Corrado, Domenico; Masotti, Andrea; Gatti, Mauro.

In: Current Opinion in Cardiology, Vol. 16, No. 1, 30.01.2001, p. 8-16.

Research output: Contribution to journalReview article

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AU - Naccarella, Franco

AU - Naccarelli, Gerald

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AU - Nava, Andrea

AU - Martini, Bortolo

AU - Corrado, Domenico

AU - Masotti, Andrea

AU - Gatti, Mauro

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AB - Right Ventricular Dysplasia constitutes a genetic cardiomyopathy characterized by fibrous-adipose substitution of the right and rarely of the left ventricular myocardium. This disorder is associated with ventricular arrhythmias ranging from frequent ventricular ectopic beats, nonsustained and sustained ventricular tachycardia of left bundle branch morphology and sudden death. Therefore, the syndrome has been labelled Arrhythmogenic RVD Cardiomyopathy. Diagnostic criteria, preliminary genetic data, and clinical manifestations are summarized and critical addressed, using data from the literature and from our own experience. The most important aspects of the ECG in this syndrome are reviewed and stressed with particular attention to initial versus advanced clinical subsets. The typical anatomical abnormalities and biopsy or pathology material are presented.

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