Cardiac tumor in juvenile onset Behçet's disease: Case report and review of the literature

Elizabeth E. Adams, Vincent P.R. Aluquin, C. April Bingham, James R. Stone, Linda B. Pauliks

Research output: Contribution to journalArticle

8 Scopus citations

Abstract

Behçe;et's disease is a chronic multisystemic inflammatory disorder characterized by orogenital ulcerations, uveitis, and occasional cardiac involvement. This report describes an atypical presentation of pediatric Behçet's disease with pulmonary emboli and a cardiac mass. A 16-year-old boy with a 2-year history of oral ulcers presented with weight loss, fever, joint pain, and a large tumor adhering to the free wall of the heart's right ventricle. Surgical biopsy demonstrated endomyocarditis with thrombus formation and led to the diagnosis. At the 2-year follow-up evaluation, intracardiac thrombus and pulmonic emboli had not recurred. Symptom control with immunosuppressive therapy was good.

Original languageEnglish (US)
Pages (from-to)277-279
Number of pages3
JournalPediatric cardiology
Volume31
Issue number2
DOIs
StatePublished - Feb 1 2010

All Science Journal Classification (ASJC) codes

  • Pediatrics, Perinatology, and Child Health
  • Cardiology and Cardiovascular Medicine

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