Congenital tracheal stenosis with unilateral pulmonary agenesis

Thomas R. Weber, Robert H. Connors, Thomas Tracy

Research output: Contribution to journalArticle

33 Citations (Scopus)

Abstract

Congenital tracheal stenosis with unilateral pulmonary agenesis is a rare and frequent fatal combination. In an 8-year period, 5 infants (ages 2 to 6 months) with these anomalies were treated. The presenting signs and symptoms consisted of wheezing, stridor, and tachypnea and included frank respiratory failure requiring emergency therapy in several patients. The operative repair consisted of segmental resection and anastomosis in one patient, and rib-cartilage tracheoplasty in the other four. Two infants died, one of cerebral hypoxia, and the other of aortotracheal fistula. Long-term follow-up in the three survivors is satisfactory.

Original languageEnglish (US)
Pages (from-to)70-74
Number of pages5
JournalAnnals of surgery
Volume213
Issue number1
DOIs
StatePublished - Jan 1 1991

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Respiratory Sounds
Tachypnea
Brain Hypoxia
Emergency Treatment
Ribs
Respiratory Insufficiency
Signs and Symptoms
Fistula
Cartilage
Survivors
Lung agenesis
Tracheal agenesis

All Science Journal Classification (ASJC) codes

  • Surgery

Cite this

Weber, Thomas R. ; Connors, Robert H. ; Tracy, Thomas. / Congenital tracheal stenosis with unilateral pulmonary agenesis. In: Annals of surgery. 1991 ; Vol. 213, No. 1. pp. 70-74.
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Congenital tracheal stenosis with unilateral pulmonary agenesis. / Weber, Thomas R.; Connors, Robert H.; Tracy, Thomas.

In: Annals of surgery, Vol. 213, No. 1, 01.01.1991, p. 70-74.

Research output: Contribution to journalArticle

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