Abstract
Purpose: We summarize the literature and present our experience with genitourinary manifestations of the Klippel-Trénaunay syndrome, which can lead to challenging management problems. Materials and Methods: We report on 2 patients with genitourinary manifestations of the Klippel-Trénaunay syndrome and performed a MEDLINE review of the literature using the key words "Klippel-Trénaunay," "vascular malformation" and "genitourinary." Results: Genitourinary manifestations were cited in 18 articles, including 1,174 cases of the Klippel-Trénaunay syndrome, detailing the presentation and management of bladder, external genitalia and retroperitoneal involvement in the Klippel-Trénaunay syndrome. The overall genitourinary symptoms in patients with the Klippel-Trénaunay syndrome seem to occur in the more severe cases and usually involve cutaneous vascular malformations of the trunk, pelvis and genitalia. Conclusions: Intra-abdominal and intrapelvic extension of the vascular malformations of the Klippel-Trénaunay syndrome frequently occurs concurrently with the lower abdominal, pelvic cutaneous involvement of the external genitalia, as in our 2 cases and in our review of the literature. These data provide a better understanding of the spectrum of genitourinary manifestations in the Klippel-Trénaunay syndrome and provide insight for the clinician to formulate individual therapies for these patients.
| Original language | English (US) |
|---|---|
| Pages (from-to) | 1418-1420 |
| Number of pages | 3 |
| Journal | Journal of Urology |
| Volume | 166 |
| Issue number | 4 |
| DOIs | |
| State | Published - Jan 1 2001 |
Fingerprint
All Science Journal Classification (ASJC) codes
- Urology
Cite this
}
Klippel-Trénaunay syndrome : 2 Case reports and a review of genitourinary manifestations. / Furness, P. D.; Barqawi, A. Z.; Bisignani, G.; Decter, Ross.
In: Journal of Urology, Vol. 166, No. 4, 01.01.2001, p. 1418-1420.Research output: Contribution to journal › Article
TY - JOUR
T1 - Klippel-Trénaunay syndrome
T2 - 2 Case reports and a review of genitourinary manifestations
AU - Furness, P. D.
AU - Barqawi, A. Z.
AU - Bisignani, G.
AU - Decter, Ross
PY - 2001/1/1
Y1 - 2001/1/1
N2 - Purpose: We summarize the literature and present our experience with genitourinary manifestations of the Klippel-Trénaunay syndrome, which can lead to challenging management problems. Materials and Methods: We report on 2 patients with genitourinary manifestations of the Klippel-Trénaunay syndrome and performed a MEDLINE review of the literature using the key words "Klippel-Trénaunay," "vascular malformation" and "genitourinary." Results: Genitourinary manifestations were cited in 18 articles, including 1,174 cases of the Klippel-Trénaunay syndrome, detailing the presentation and management of bladder, external genitalia and retroperitoneal involvement in the Klippel-Trénaunay syndrome. The overall genitourinary symptoms in patients with the Klippel-Trénaunay syndrome seem to occur in the more severe cases and usually involve cutaneous vascular malformations of the trunk, pelvis and genitalia. Conclusions: Intra-abdominal and intrapelvic extension of the vascular malformations of the Klippel-Trénaunay syndrome frequently occurs concurrently with the lower abdominal, pelvic cutaneous involvement of the external genitalia, as in our 2 cases and in our review of the literature. These data provide a better understanding of the spectrum of genitourinary manifestations in the Klippel-Trénaunay syndrome and provide insight for the clinician to formulate individual therapies for these patients.
AB - Purpose: We summarize the literature and present our experience with genitourinary manifestations of the Klippel-Trénaunay syndrome, which can lead to challenging management problems. Materials and Methods: We report on 2 patients with genitourinary manifestations of the Klippel-Trénaunay syndrome and performed a MEDLINE review of the literature using the key words "Klippel-Trénaunay," "vascular malformation" and "genitourinary." Results: Genitourinary manifestations were cited in 18 articles, including 1,174 cases of the Klippel-Trénaunay syndrome, detailing the presentation and management of bladder, external genitalia and retroperitoneal involvement in the Klippel-Trénaunay syndrome. The overall genitourinary symptoms in patients with the Klippel-Trénaunay syndrome seem to occur in the more severe cases and usually involve cutaneous vascular malformations of the trunk, pelvis and genitalia. Conclusions: Intra-abdominal and intrapelvic extension of the vascular malformations of the Klippel-Trénaunay syndrome frequently occurs concurrently with the lower abdominal, pelvic cutaneous involvement of the external genitalia, as in our 2 cases and in our review of the literature. These data provide a better understanding of the spectrum of genitourinary manifestations in the Klippel-Trénaunay syndrome and provide insight for the clinician to formulate individual therapies for these patients.
UR - http://www.scopus.com/inward/record.url?scp=0034821154&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=0034821154&partnerID=8YFLogxK
U2 - 10.1016/S0022-5347(05)65798-9
DO - 10.1016/S0022-5347(05)65798-9
M3 - Article
C2 - 11547101
AN - SCOPUS:0034821154
VL - 166
SP - 1418
EP - 1420
JO - Journal of Urology
JF - Journal of Urology
SN - 0022-5347
IS - 4
ER -