Manifestazioni otologiche della sindrome di susac

Translated title of the contribution: Otologic manifestations of susac syndrome

V. A. Patel, M. Dunklebarger, T Thomas Zacharia, Huseyin Isildak

Research output: Contribution to journalArticle

Abstract

Susac syndrome, a rare autoimmune disorder first described as a classic triad (encephalopathy, branch retinal artery occlusion, and sensorineural hearing loss) in 1979 by renowned physician John O. Susac, has been an advancing area of clinical interest and scientific research over the last several decades. This comprehensive review aims to succinctly highlight the breadth and detail of this enigmatic disease, with a primary focus on otologic manifestations. Topics discussed include epidemiology, pathophysiology, clinical manifestations, differential diagnoses, classification schema, laboratory investigations, characteristic audiometric findings, high-yield radiographic imaging, temporal bone histopathology, treatment strategies and overall prognosis.

Original languageItalian
Pages (from-to)544-553
Number of pages10
JournalActa Otorhinolaryngologica Italica
Volume38
Issue number6
DOIs
StatePublished - Dec 1 2018

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Susac Syndrome
Retinal Artery Occlusion
Sensorineural Hearing Loss
Temporal Bone
Brain Diseases
Epidemiology
Differential Diagnosis
Physicians
Research
Therapeutics

All Science Journal Classification (ASJC) codes

  • Otorhinolaryngology

Cite this

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Manifestazioni otologiche della sindrome di susac. / Patel, V. A.; Dunklebarger, M.; Zacharia, T Thomas; Isildak, Huseyin.

In: Acta Otorhinolaryngologica Italica, Vol. 38, No. 6, 01.12.2018, p. 544-553.

Research output: Contribution to journalArticle

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