Surgical decompression of Chiari I malformation for isolated progressive sensorineural hearing loss

G. D. Johnson, R. E. Harbaugh, S. B. Lenz

Research output: Contribution to journalArticle

15 Citations (Scopus)

Abstract

Progressive sensorineural hearing loss has been associated with Chiari type I malformation. Retrocochlear features on auditory brainstem response testing have been reported; however, debate exists over the exact location of the defect. Surgical decompression may be beneficial if brainstem or vascular compression have played a significant role in the pathophysiology of the hearing loss. Lack of specific audiologic data before and after surgical decompression has kept surgical decision making theoretic. This report presents the case of a 10-year-old boy with a progressive, asymmetric sensorineural hearing loss without other neurologic abnormalities. He underwent a posterior fossa decompression that resulted in stable hearing over the 2 years he was followed postoperatively. Preoperative and postoperative audiologic and evoked response features are described, and the rationale for operating with symptoms limited to hearing loss is discussed.

Original languageEnglish (US)
Pages (from-to)634-638
Number of pages5
JournalAmerican Journal of Otology
Volume15
Issue number5
StatePublished - Jan 1 1994

Fingerprint

Surgical Decompression
Sensorineural Hearing Loss
Hearing Loss
Arnold-Chiari Malformation
Nervous System Malformations
Brain Stem Auditory Evoked Potentials
Decompression
Hearing
Brain Stem
Blood Vessels
Decision Making

All Science Journal Classification (ASJC) codes

  • Otorhinolaryngology

Cite this

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abstract = "Progressive sensorineural hearing loss has been associated with Chiari type I malformation. Retrocochlear features on auditory brainstem response testing have been reported; however, debate exists over the exact location of the defect. Surgical decompression may be beneficial if brainstem or vascular compression have played a significant role in the pathophysiology of the hearing loss. Lack of specific audiologic data before and after surgical decompression has kept surgical decision making theoretic. This report presents the case of a 10-year-old boy with a progressive, asymmetric sensorineural hearing loss without other neurologic abnormalities. He underwent a posterior fossa decompression that resulted in stable hearing over the 2 years he was followed postoperatively. Preoperative and postoperative audiologic and evoked response features are described, and the rationale for operating with symptoms limited to hearing loss is discussed.",
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Surgical decompression of Chiari I malformation for isolated progressive sensorineural hearing loss. / Johnson, G. D.; Harbaugh, R. E.; Lenz, S. B.

In: American Journal of Otology, Vol. 15, No. 5, 01.01.1994, p. 634-638.

Research output: Contribution to journalArticle

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